Indian Journal of Pathology and Microbiology

CASE REPORT
Year
: 2018  |  Volume : 61  |  Issue : 1  |  Page : 94--97

Sporadic lymphangioleiomyomatosis with multiple atypical features: A case report and literature review


Xiaokang Wang1, Fei Su2, Fenfang Zhou1, Maohui Feng1 
1 Department of Oncology, Zhongnan Hospital of Wuhan University, Wuhan, Hubei, China
2 Department of Oncology, The First Affiliated Hospital of Lanzhou University, Lanzhou, Gansu, China

Correspondence Address:
Maohui Feng
Department of Oncology, Zhongnan Hospital of Wuhan University, No 169, Donghu Road, Wuchang District, Wuhan 430071
China

Lymphangioleiomyomatosis (LAM) is a rare, genetically determined, progressive interstitial lung disease, which almost exclusively affects women, especially at the childbearing age. The initial symptoms and radiographic changes in a patient with LAM are always associated with the respiratory system. Here, we present a case of mediastinal and abdominal LAM of a 22-year-old male, where LAM cells are negative for human melanoma black-45 ( HMB-45). The report of this uncharacterized LAM case will make a significant contribution to the realization of LAM associated clinical features, diagnostic approaches, and its afterward treatments.


How to cite this article:
Wang X, Su F, Zhou F, Feng M. Sporadic lymphangioleiomyomatosis with multiple atypical features: A case report and literature review.Indian J Pathol Microbiol 2018;61:94-97


How to cite this URL:
Wang X, Su F, Zhou F, Feng M. Sporadic lymphangioleiomyomatosis with multiple atypical features: A case report and literature review. Indian J Pathol Microbiol [serial online] 2018 [cited 2023 Feb 8 ];61:94-97
Available from: https://www.ijpmonline.org/article.asp?issn=0377-4929;year=2018;volume=61;issue=1;spage=94;epage=97;aulast=Wang;type=0