Pigmented medulloepithelioma of the optic nerve: A challenging diagnostic entity El Mehdi T, Siham C, Imane K, Noufissa B, Amal B, - Indian J Pathol Microbiol

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CASE REPORT

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Pigmented medulloepithelioma of the optic nerve: A challenging diagnostic entity Tiabi El Mehdi¹, Chariba Siham², Kamaoui Imane³, Benajiba Noufissa⁴, Bennani Amal¹ ¹ Department of Pathology, Mohammed VI University Hospital, Oujda; Faculty of Medicine and Pharmacy of Oujda, Mohammed First University of Oujda, Morocco ² Department of Ophtalmology, Mohammed VI University Hospital, Oujda; Faculty of Medicine and Pharmacy of Oujda, Mohammed First University of Oujda, Morocco ³ Department of Radiology, Mohammed VI University Hospital, Oujda; Faculty of Medicine and Pharmacy of Oujda, Mohammed First University of Oujda, Morocco ⁴ Department of Pediatrics, Mohammed VI University Hospital, Oujda; Faculty of Medicine and Pharmacy of Oujda, Mohammed First University of Oujda, Morocco Correspondence Address: Tiabi El Mehdi, Mohammed VI University Hospital, Oujda Morocco Source of Support: None, Conflict of Interest: None DOI: 10.4103/ijpm.ijpm_116_22

Because of its rarity, the diagnosis of optic nerve medulloepithelioma poses a real diagnostic challenge. Medulloepithelioma is a congenital tumor that derives from the primitive medullary epithelium present in the neural tube and the optic vesicle. Its classical location is the ciliary body. Cases of retinal or optic nerve locations have been rarely reported in the literature. Only 11 cases have been published in the English literature. Herein, we report the case of a 2-year-old boy who underwent enucleation of the right eye for a presumed diagnosis of right-eye retinoblastoma, based on the presence of leukocoria on ophthalmological examination. Pathological examination showed an optic nerve medulloepithelioma. A review of the literature is also discussed in our work.

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    -  El Mehdi T
    -  Siham C
    -  Imane K
    -  Noufissa B
    -  Amal B

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