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Plexiform fibromyxoma of the stomach: An underrecognized entity!
Surbhi Goyal1, Patricia Beso1, Rahul Khullar2, Puja Sakhuja1
1 Department of Pathology, Govind Ballabh Pant Institute of Post Graduate Medical Education and Research (GIPMER), New Delhi, India
2 Department of Surgery, Govind Ballabh Pant Institute of Post Graduate Medical Education and Research (GIPMER), New Delhi, India
Correspondence Address:
Puja Sakhuja,
Director Professor and Head, Department of Pathology, Govind Ballabh Pant Institute of Post Graduate Medical Education & Research (GIPMER), New Delhi
India
 Source of Support: None, Conflict of Interest: None DOI: 10.4103/IJPM.IJPM_480_20
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Plexiform fibromyxoma (PF) is a recently described rare type of mesenchymal tumor of the stomach with only 123 cases reported in the literature. It is characterized by a peculiar plexiform growth pattern, myxoid stroma with arborizing microvasculature, and spindle-shaped myofibroblastic cells. We herein report a case of gastric PF in a 15-year-old boy, mimicking a gastrointestinal stromal tumor (GIST) due to overlapping clinicoradiological features. Distinct pathological and immunohistochemical features of PF do aid in distinction from GIST and other mesenchymal entities. Diagnosis is crucial as surgical resection is the mainstay of treatment unlike aggressive management in GIST. It is a benign entity with no local recurrence or distant metastasis reported so far, but confirmation of the same requires longitudinal observational studies with a larger sample size.
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