| CASE REPORT |
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| Year : 2008 | Volume
: 51
| Issue : 4 | Page : 504-506 |
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Cutaneous angiosarcoma in a patient with xeroderma pigmentosum
Raman Arora, Alok Sharma, Ruchika Gupta, M Vijayaraghavan
Department of Pathology, All India Institute of Medical Sciences, New Delhi 110 029, India
Correspondence Address:
Alok Sharma
Department of Pathology, All India Institute of Medical Sciences, New Delhi 110 029
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0377-4929.43741
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Xeroderma pigmentosum (XP) is a rare, autosomal recessive disorder characterized by photosensitivity, cutaneous pigmentary changes, premature skin ageing and development of various cutaneous and internal malignancies at an early age as a result of a defect in nucleotide excision repair following ultraviolet light exposure. Cutaneous angiosarcomas are aggressive neoplasms that are rarely associated with XP. In this communication, we report the case of a 40-year-old male patient with XP who developed an angiosarcoma of the face and discuss the implications of this association in view of recent developments in this field. |
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